Mediterr. J. Otol 2007; 3:(1)

Bilateral Fibrous Dysplasia of the Temporal Bone in a Patient with a Unilateral Giant Cholesteatoma

Harun Dogru, Mustafa Tuz, Hasan Yasan, Giray Aynali, Orhan Oyar

Departments of Otolaryngology and Radiodiagnostics, Suleyman Demirel University School of Medicine, Isparta, Turkey hyasan@med.sdu.edu.tr

Fibrous dysplasia, which is a localized pathologic disorder of bone, is characterized by the abnormal proliferation of fibrous tissue that is interspersed with normal or immature bone. Involvement of the temporal bone, which is usually unilateral, develops in only 18% of all patients with fibrous dysplasia and occurs more frequently in a monostotic rather than a polyostotic form. To our knowledge, only 3 patients with bilateral temporal bone involvement have been reported in the literature. We present the case of a patient with minimal symptoms who was diagnosed as having bilateral monostotic fibrous dysplasia of the temporal bones and a concomitant giant cholesteatoma.