Mediterr J Otol 2006:2(1): 47-51
Ozan Seymen Sezen, Utku Kubilay, Temel Coşkuner, Mahmut Özkırış, Seref Ünver
Department of Otolaryngology, Head and Neck Surgery, Dr. Lütfi Kırdar Kartal Training and Research Hospital, Istanbul, Turkey dramahmut@yahoo.com
Mondini dysplasia represents a developmental arrest during the embryogenesis of the inner ear. The malformation, commonly associated with deafness, is frequently heralded by meningitis secondary to communication of the middle ear with the subarachnoid space. Early recognition and successful repair of the cerebrospinal fluid leak is important to avoid the sequelae or repeated episodes of meningitis.
We report a case of a 5-year-old girl in whom Mondini dysplasia presented initially with recurrent pyogenic bacterial meningitis. This case is being reported for its rarity and to increase awareness among physicians regarding the possibility of Mondini dysplasia in children with recurrent pyogenic meningitis and sensorineural deafness.